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Summary ExpressionExpr. PhenotypesPheno. Gene Literature (1)Lit. (1) GO Terms (44)GO (44) Nucleotides (115)Nucl. (115) Proteins (41)Prot. (41) Interactants (236)Interact. (236) Wiki
XB-GENEPAGE-1013274
???displayGene.symbol???:
 lonp1

???displayGene.name???: 
lon peptidase 1, mitochondrial

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( Nomenclature history )

???displayGene.geneFunction???
Mitochondrial ATP-dependent protease PIM1/LON

AI Protein Function :
lonp1 encodes a mitochondrial AAA+ protease that hydrolyzes ATP to degrade misfolded or damaged proteins in the mitochondrial matrix, contributes to mitochondrial DNA maintenance and supports oxidative...[+]


InterPro :
ATPase AAA core, Peptidase S16 AS, Ribosomal S5 D2-typ fold, PUA-like sf, [+]

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Diseases: 


Disease Ontology:
CODAS syndrome

MIM:
CODAS SYNDROME

External Links:
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???displayGene.expression???                  Development Stages                                               Embryonic Tissues                                                                Adult Tissues
More Information
Xenbase Expression Details In situ images Single cell data at SPRING In situ: RNA-Seq:


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